Tachypnea of infancy as the first sign of Sanfilippo syndrome.

نویسندگان

  • Jackie Chiang
  • Julian Raiman
  • Ernest Cutz
  • Melinda Solomon
  • Sharon Dell
چکیده

This report describes the first known case of Mucopolysaccharidosis type IIIA presenting with respiratory symptoms and characteristic lung pathology. This case highlights under-recognized areas of systemic involvement and earlier modes of presentation in lysosomal storage disorders as well as the importance of investigating infants who have persistent tachypnea.

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عنوان ژورنال:
  • Pediatrics

دوره 134 3  شماره 

صفحات  -

تاریخ انتشار 2014